Descriptive analysis of cystic fibrosis patients followed by the Pediatric Pulmonology Unit of a university hospital in Porto Alegre-RS
Autor/a
Gava Chakr, Valentina C. B.
Vendrusculo, Fernanda Maria
Tomedi Leites, Gabriela
Fagundes Donadio, Márcio Vinícius
Frescura Paim, Taísa
Cauduro Marostica, Paulo José
Rúbia Silveira, Mara
Data de publicació
2006ISSN
1980-6108
Resum
Aims: To provide a descriptive analysis of patients followed in a local cystic fibrosis treatment center and compare the collected data with those found in the literature. Methods: Relevant data for clinical follow-up of cystic fibrosis patients were used for analysis and correlation. Results: Twenty six male and twenty two female patients were studied. From 48 patients, 89,6% presented with pancreatic insufficiency and 29,1% had at least one positive culture to Pseudomonas aeruginosa in the last 6 months. The patients colonized by P. aeruginosa and the ones with pancreatic insufficiency presented with worse values for forced expiratory volume in one second (FEV1). The pancreatic insufficiency group (84 versus 112%; p = 0,005) and the patients colonized by P. aeruginosa (75 versus 85%; p = 0,006) had lower pulmonary function parameters. Conclusions: The data from our study show that this group of patients presents in accordance with data available from literature, considering the analysed features of the disease. However, there is a marked exception in the time of diagnosis, which is still very late in Brazil.
Tipus de document
Article
Versió del document
Versió publicada
Llengua
Portuguès
Matèries (CDU)
61 - Medicina
616.2 - Patologia de l'aparell respiratori
Paraules clau
Fibrosi quística
Diagnòstic
Dietoterapia
Nen
Infant
Adolescent
Espirometria
Fibrosis quística
Diagnóstico
Dietoterapia
Niño
Infante
Adolescente
Espirometría
Cystic fibrosis
Diagnosis
Diet therapy
Boy
Infant
Teenager
Spirometry
Pàgines
6
Publicat per
Electronic Journal Publishing System
Col·lecció
16; 3
Publicat a
Scientia Medica
Citació
Gava Chakr, Valentina C. B.; Vendrusculo, Fernanda Maria; Tomedi Leites, Gabriela [et al.]. Descriptive analysis of cystic fibrosis patients followed by the Pediatric Pulmonology Unit of a university hospital in Porto Alegre-RS. Scientia Medica, 2006, 16(3), 103-108. Disponible en: <https://revistaseletronicas.pucrs.br/ojs/index.php/scientiamedica/article/view/1617>. Fecha de acceso: 8 abr. 2022.
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- Ciències de la Salut [740]
Drets
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